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FBN1, Mouse, Clone: 3H6, Abnova™
Mouse monoclonal antibody raised against a partial recombinant FBN1.
Supplier: Abnova Corporation H00002200M01
Description
This gene encodes a member of the fibrillin family. The encoded protein is a large, extracellular matrix glycoprotein that serve as a structural component of 10-12nm calcium-binding microfibrils. These microfibrils provide force bearing structural support in elastic and nonelastic connective tissue throughout the body. Mutations in this gene are associated with Marfan syndrome, isolated ectopia lentis, autosomal dominant Weill-Marchesani syndrome, MASS syndrome, and Shprintzen-Goldberg craniosynostosis syndrome. [provided by RefSeq
Sequence: SNKVRILELLPALTTLTNHNRYLIESGNEDGFFKINQKEGISYLHFTKKKPVAGTYSLQISSTPLYKKKELNQLEDKYDKDYLSGELGDNLKMKIQVLLHSpecifications
| FBN1 | |
| Monoclonal | |
| Unconjugated | |
| PBS with no preservative; pH 7.4 | |
| NM_000138 | |
| FBN1 | |
| FBN1 (NP_000129, 2772 a.a. ∼ 2871 a.a) partial recombinant protein with GST tag. MW of the GST tag alone is 26 KDa. | |
| 100 μg | |
| Primary | |
| Human | |
| Antibody | |
| IgG2a κ |
| ELISA, Immunohistochemistry (PFA fixed), Western Blot | |
| 3H6 | |
| Mouse monoclonal antibody raised against a partial recombinant FBN1. | |
| FBN1 | |
| FBN/MASS/MFS1/OCTD/SGS/WMS | |
| Mouse | |
| Affinity chromatography | |
| RUO | |
| 2200 | |
| Store at -20°C or lower. Aliquot to avoid repeated freezing and thawing. | |
| Liquid |